Nilay BAŞ İKİZOĞLU1, Emine ATAĞ1, Almala Pınar ERGENEKON1, Cansu YILMAZ YEĞİT1, Yasemin GÖKDEMİR1, Ela ERDEM ERALP1, Ayşim BÜGE ÖZ2, Bulent KARADAG1

1Department of Pediatrics, Division of Pediatric Pulmonology, Marmara University School of Medicine, Istanbul, Turkey
2Department of Pathology, Istanbul University Cerrahpaşa Faculty of Medicine, Istanbul, Turkey

Keywords: Connective tissue disease, hemoptysis, pediatrics, pulmonary

Abstract

Behçet’s disease (BD) is a rare autoimmune and chronic inflammatory vasculitis, characterized by relapsing episodes of oral aphthous and genital ulcers, skin lesions, ocular lesions and vascular involvement. Pulmonary artery involvement is rare in BD but it carries a high mortality risk. In this article, we report a 15-year-old male patient presented with a two-month history of hemoptysis, cough, fewer and weight loss. On physical examination, auscultation revealed decreased breath sounds at left lung base. Bronchoscopy showed narrowed left lower lobe bronchus due to the external compression. Computed tomography angiography revealed multiple bilateral pulmonary artery aneurysms. Pathergy test was positive and he was diagnosed with BD. BD should be considered in the differential diagnosis of childhood hemoptysis.