Wegener's Granulomatosis Presenting With an Isolated Paranasal Sinus Involvement in a Child
Ghaniya DAAR, 1 Ali Bülent CENGİZ, 2 Ateş KARA, 2 Rezan TOPALOĞLU, 2 Ömer Taşkın YÜCEL, 3 İsmail DURSUN4
1Department of Pediatrics, Medical Faculty of Bozok University, Yozgat, Turkey
2Department of Pediatrics, Medical Faculty of Hacettepe University, İhsan Doğramacı Children's Hospital, Ankara, Turkey
3Department of Otolaryngology, Medical Faculty of Hacettepe University, Ankara, Turkey
4Department of Pediatrics, Medical Faculty of Erciyes University, Kayseri, Turkey
Keywords: Child; paranasal sinus; Wegener's granulomatosis
Abstract
Wegener's granulomatosis which is rarely seen in children is an idiopathic necrotizing granulomatous vasculitis, affecting primarily paranasal sinuses, nasopharynx, lungs, kidneys and joints. In this article, we report a very rare case of eight-year-old boy presenting with Wegener's granulomatosis of paranasal sinuses without lung, kidney and any other organ involvement. We discuss the diagnosis, treatment and the differential diagnosis of paranasal sinus involvement in Wegener's granulomatosis in the light of literature data.